KMID : 0371319950490060906
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Journal of the Korean Surgical Society 1995 Volume.49 No. 6 p.906 ~ p.910
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A Case of Rhabdomyosarcoma of the Liver in Child
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Abstract
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Rhabdomyosarcoma of the biliary tree in childhood is extremely rare. It was reported about 40 cases in the world. In Korea there are a few reports on rhabdomyosarcoma in biliary tree, but no report on rhabdomyosarcoma developed in the liver. This
is the
first case report on rhabdomyosarcoma of the liver in Korea. A 29 months old female presented with intermitent abdominal pain, and revealed palpable mass in epigastric area. On CAT scan, a single large mass(6.9¡¿7.3¡¿4.7cm) was noted in the left
lobe of
the liver which was confirmed after left hepatic lobectomy. Cut surgace fevealed a relatively well demarcated, white homogenous tumor without necrosis or hemorrhage(See Fig. 2) . Microscopic examination revealed malignant mesenchymal tumor of
liver
composed of primitive round to oval cells with hyperchromatic muclei and elongated strap-shaped cells with long elongated cytoplasmic processes beneath the bile ductal epithelium. It was diagnosed as botryoid-type embryonal rhabdomyosarcoma.
After
surgery, she recelved chemotherapy 15 times over 11 months. She is in follow-up without evidence of recurrence.
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KEYWORD
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